Endometrial Stromal Sarcoma in Term Pregnancy: A Unique Case Report and Review of the Literature

Authors

  • Eva Koulaymi, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Al Zahraa Hospital, Beirut, Lebanon
  • Mayssaloun Khairallah, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Al Zahraa Hospital, Beirut, Lebanon
  • Zeinab Haroun, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Al Zahraa Hospital, Beirut, Lebanon
  • Kawthar Kassab, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Al Zahraa Hospital, Beirut, Lebanon
  • Jihad Al Hassan, MD Department of Obstetrics and Gynecology, Al Zahraa Hospital, Beirut, Lebanon | Department of Obstetrics and Gynecology, Rafik Hariri University Hospital, Beirut, Lebanon
  • Janoub Khazaal, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Rafik Hariri University Hospital, Beirut, Lebanon
  • Georges Wehbe, MD Department of Obstetrics and Gynecology, Rafik Hariri University Hospital, Beirut, Lebanon
  • Lilian Nasser, MD Department of Obstetrics and Gynecology, Lebanese University, Beirut, Lebanon | Department of Obstetrics and Gynecology, Rafik Hariri University Hospital, Beirut, Lebanon

DOI:

https://doi.org/10.38179/ijcr.v4i1.269

Keywords:

Stromal sarcoma, Pregnancy, Endometrial Anti-CD 10 receptor, Anti-estrogen receptor

Abstract

Background: Endometrial stromal sarcoma (ESS)is a rare malignancy described only in a limited number of case reports. It accounts for only 2% of all uterine tumors. 

Case Report: We describe a case of a 29-year-old pregnant lady presenting at 37 weeks of gestation in labor. A huge intra-cavitary mass was seen on bedside ultrasound upon her presentation. The patient underwent an urgent repeat cesarean section where a twenty cm uterine mass was identified after delivering the baby and the placenta. The pathology exam of the group showed low-grade endometrial stromal sarcoma with anti-CD10 and anti-estrogen receptors. A radical hysterectomy with bilateral salpingo-oophorectomy was performed two days later as the ESS was staged 1B following the post-cesarean PET scan result.

Conclusion: ESS is infrequent in young women as well as pregnant patients. This is the first case of asymptomatic endometrial stromal sarcoma in pregnancy, giving birth to a full-term baby with successful treatment.

References

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Spontaneous extrusion of the uterine mass after placental delivery

Published

2024-07-18

How to Cite

Koulaymi, E., Khairallah, M., Haroun, Z., Kassab, K., Al Hassan, J., Khazaal, J., Wehbe, G., & Nasser, L. (2024). Endometrial Stromal Sarcoma in Term Pregnancy: A Unique Case Report and Review of the Literature. International Journal of Clinical Research, 4(1), 36-39. https://doi.org/10.38179/ijcr.v4i1.269